SHARE CAPITAL AND VOTING RIGHTS IN ORPHAZYME A/S

Copenhagen, March 29, 2019 – Following a share capital increase in Orphazyme A/S (ticker: ORPHA.CO), CVR no. 32266355 (“Orphazyme”) in March 2019, the total nominal share capital of Orphazyme is DKK 19,984,799, divided into 19,984,799 shares each with a nominal value of DKK 1. Each share carries one vote at Orphazyme’s general meetings and accordingly the total number of voting rights in Orphazyme is 19,984,799.

This announcement is published pursuant to section 32 of the Danish Capital Markets Act.